Brachial plexus birth palsy is caused by trauma to the brachial plexus nerves during childbirth, often due to downward or upward traction on the arm. This can lead to muscle imbalance and contractures over time. There are three main types classified by the specific nerves involved. While some cases can be prevented, most cannot be anticipated. The majority of cases recover spontaneously within the first year, while the remaining 20% may require nerve grafting, tendon transfers, or other surgeries to improve function. Prognosis is generally good, with 80% recovering fully, but contractures and sensory loss can occasionally occur without treatment.
Brachial plexus birth palsy is caused by trauma to the brachial plexus nerves during childbirth, often due to downward or upward traction on the arm. This can lead to muscle imbalance and contractures over time. There are three main types classified by the specific nerves involved. While some cases can be prevented, most cannot be anticipated. The majority of cases recover spontaneously within the first year, while the remaining 20% may require nerve grafting, tendon transfers, or other surgeries to improve function. Prognosis is generally good, with 80% recovering fully, but contractures and sensory loss can occasionally occur without treatment.
Brachial plexus birth palsy is caused by trauma to the brachial plexus nerves during childbirth, often due to downward or upward traction on the arm. This can lead to muscle imbalance and contractures over time. There are three main types classified by the specific nerves involved. While some cases can be prevented, most cannot be anticipated. The majority of cases recover spontaneously within the first year, while the remaining 20% may require nerve grafting, tendon transfers, or other surgeries to improve function. Prognosis is generally good, with 80% recovering fully, but contractures and sensory loss can occasionally occur without treatment.
Brachial plexus injury->stretch during birth that is
caused by downward or upward traction on the arm
Secondarily, the muscles and bones of the upper extremity become contracted or deformed over time because of the resultant muscle imbalance may not be detected until the baby tries to use the extremity Classification : Type I (Erb palsy): Injury to roots 4-6 of the cervical spine Type II (whole-brachial plexus palsy): C4-T1 involved; also known as Erb-Duchenne-Klumpkepalsy Type III (Klumpke palsy): C8-T1 involved
General Prevention Sometimes obstetricians will advise a caesarean section if a baby seems extremely large or cephalopelvic disproportion is present. Not all cases can be anticipated or prevented
Epidemiology Incidence Currently, the incidence is 0.8 per 1,000 live births (2). This figure is a decline from the rate in 1900, when it was reported twice as often. The change most likely results from improved obstetric care. Erb palsy is ~4 times as common as Klumpke palsy. No recognized difference exists in incidence between boys and girls.
Risk Factors Fetal malposition Shoulder dystocia Cephalopelvic disproportion High birth weight: Maternal diabetes Use of forceps in delivery
Pathophysiology Pathologic findings vary from stretch to disruption of the nerves of the brachial plexus (3). The injury may occur at the cervical foramen as the nerves exit the spinal canal (poorer prognosis), or farther down in the neck and shoulder. Secondary muscle atrophy and contracture ensues.
Etiology Erb palsy results from downward traction on the shoulder or arm or lateral traction against the neck. Klumpke palsy is secondary to upward traction on the arm. Both occur because of the force needed in a difficult extraction.
Associated Conditions High birth weight Gestational diabetes
Diagnosis
Signs and Symptoms Decreased active use of the extremity Arm held in internal rotation (2) Loss of full active or passive external rotation Inability to abduct (raise) the shoulder Atrophy of the involved muscles (late) (Fig. 1) Elbow flexion contracture Possible Horner syndrome in Klumpke palsy The condition is not painful. A loss of sensation may be noted with complete plexus injuries.
History Decreased infant arm movements sometimes are noted from birth. In other cases, more subtle decreases in shoulder movement or presence of arm contracture may not be noted until later. Physical Exam Physical examination is the primary means of diagnosis. Palpate for tenderness over the clavicle, proximal humerus, and ribs. Test sensation by responses to light touch or pinch. Test the function of all muscles in the shoulder, elbow, and hand by stimulation and observation. In patients with Erb palsy, the shoulder is internally rotated and lacks external rotation and abduction. In Klumpke palsy, loss of finger and interosseous function occurs.
12 17 13 17 Tests Imaging Plain radiographs often are indicated at birth to rule out other injuries that may cause decreased movement of the infant's arm (clavicle fracture, proximal humerus fracture); such injuries may coexist with brachial plexus birth palsy. At the time of late reconstruction in a child >4 years old who has residual shoulder imbalance, plain radiographs and CT scans are indicated to assess the shape of the glenohumeral joint.
Diagnostic Procedures/Surgery An electromyogram should be obtained if no clinical return of deltoid or biceps function occurs by 36 months of age. Lack of reinnervation may be a relative indication for surgery. Cervical myelography may be helpful for diagnosing the level of injury. Meningoceles seen at the root levels in the cervical spinal cord indicate that roots were avulsed from the cord, and the prognosis is poor. A finding of meningoceles indicates that different strategies may be needed at surgery.
Differential Diagnosis Clavicle fracture: Usually painful to palpation Some shoulder motion may be elicited. Proximal humeral physeal fracture: Same findings as clavicle fracture, with tenderness over the proximal humerus; the abnormality may not show on radiographs because the proximal humerus is not ossified at birth. Ultrasound or MRI studies may be diagnostic, as are plain films 710 days later. Septic arthritis of the shoulder: May cause pseudoparalysis Fever in the newborn may not be pronounced.
Treatment General Measures Parents should stretch the infant's arm several times a day as directed by the occupational therapist (13). The patient should be referred to a specialized pediatric orthopaedic surgeon for monitoring and decision-making. Observation and passive ROM are indicated for the newborn; 80% of patients recover spontaneously by 1 year of age (4). Splinting is not necessary, but continued follow-up is needed. Surgery is indicated for the remaining 20% of patients, with grafting of the injured nerves (if no meningoceles are present and the elapsed time is not >2 years) or with tendon transfers to improve muscle balance .
Activity No restrictions Encourage passive ROM.
Special Therapy Physical Therapy An occupational therapist is helpful in teaching the parents how to stretch and what contractures to watch for. Splinting is not needed, but stretching and passive ROM are encouraged.
Surgery Nerve repair/reconstruction: May be performed with an operative microscope with direct repair or grafting of the injured nerves if the patient's function does not return in ~6 months. The exact timing is controversial. Tendon transfers may be performed later to restore external rotation to the shoulder. Release of the tight internal rotators also may be indicated. Humeral osteotomy is another way to restore an externally rotated position. Several muscle transfers are available to restore elbow flexion, most notably the latissimus transfer. Transfers for finger and wrist function are least commonly needed.
Follow-up
Issues for Referral It is important to refer the baby with brachial birth palsy to an orthopaedic surgeon with an interest in this condition because it is a specialized field. Prognosis 80% of patients with brachial plexus birth palsy recover spontaneously. Surgery may help many of the remainder. Complications Contracture of shoulder, elbow, or wrist Affected extremity smaller in length and girth Sensory loss Shoulder dislocation Patient Monitoring The patient should be seen approximately every 23 months to look for return of function and to plan for appropriate diagnostic testing.