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Ventricle
Mediana Sutopo Liedapraja
PPDS Tahap 2A
Departemen Obstetri dan
Ginekologi
FKUI-RSCM
Hypoplastic Right
Ventricle
Complex cardiac
malformation
Prenatal sonographic
features: Pulmonary atresia
with an intact ventricular
septum, tricuspid atresia,
tricuspid regurgitation, and
hypoplasia of right
ventricular walls.
Significant disproportion in
size between two
ventricular cavities.
Differential Diagnosis
Fetal Echocardiography only one ventricle is clearly visible
DD/
- Hypoplastic left heart syndrome
- Right sided cardiac masses
- Pulmonary stenosis
- Univentricular heart
Doppler echocardiography absence of antegrade flow through
pulmonary valve ( confirm presence of complete pulmonary atresia).
Treatment
Grup A
Grup C
Grup B
Severe hypoplasia
and infundibulum
completely atretic
Moderate hypoplasia
Ductal dependent
- Pulmonary valvotomy
- Prolonged
prostaglandin infusion
- PDA Stenting or
Blalock-Taussig shunt
Infundibular hypoplasia
(laser assisted or
radiofrequency)
-Stenting of the PDA
- Balloon atrial
septostomy
Hypoplastic Left
Ventricle
Postnatal
Left to right shunting
Returning oxygenated
blood from pulmonary vein
through a patent foramen
ovale into right atrium.
Right ventricle provide both
pulmonary and systemic
circulation
Mitral valve is hypoplastic
Tricuspid valve is often
large and regurgitant
Postnatal Therapy
Infusion prostaglandin E1
Surgical neonatal heart
transplantation
Norwood procedure ( 3 stages)
Survival after surgery 55-65%
Palliative
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